Wegeners granulomatosis is a systemic necrotizing vasculitis that af fects small. Its hallmark features include necrotizing granulomatous inflammation and pauciimmune vasculitis in small and mediumsized blood vessels see the images below. January 2004 1chu hopital cochin, 27 rue du faubourg saintjacques, 75014 paris, france loic. A multisystemic disease of a complex genetic background. Ecr 2012 c1093 imaging manifestation of wegener granulomatosis. Granulomatosis with polyangiitis gpa, previously known as wegener s granulomatosis wg, is an extremely rare longterm systemic disorder that involves the formation of granulomas and inflammation of blood vessels vasculitis. Jara quezada lj, saavedrasalinas ma, veralastra o, espinoza lr.
Initially described by klinger in 1931 and by wegener in 1936, wegeners granulomatosis is a small and medium vessels vasculitis. Professor loic guillevin1,2, doctor alfred mahr creation date. Granulomatosis with polyangiitis gpa, formerly wegener. It is characterized by inflammation of the blood vessels vasculitis leading to damage in any number of organs. Kites 2012 malayalam full movie watch online download. Abstract wegeners granulomatosis is a necrotizing granulomatous vasculitis that affects the upper respiratory tract, lower and glomerul i. Enfermedades autoinmunes sistemicas reumatologicas. Granulomatosis with polyangiitis, a new nomenclature for wegeners. Oct 09, 2019 granulomatosis with polyangiitis gpa, formerly known as wegener granulomatosis, is a rare multisystem autoimmune disease of unknown etiology.
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